Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis Type I : Unusual Presentation of Intraabdominal or Intrathoracic Mass
Jong Gwang Kim, Woo Jin Sung, Dong Hwan Kim, Young Hwan Kim, Sang Kyun Sohn, Kyu Bo Lee
Korean J Intern Med. 2005;20(1):100-104. Published online March 31, 2005
A malignant peripheral nerve sheath tumor (MPNST) is an extremely rare soft tissue tumor in the general population. On the other hand, there is a higher incidence of MPNST in patients with neurofibromatosis type I (von Recklinghausen's disease). The common sites are the extremities, trunk, head a..
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